Understanding Rett Syndrome: A Practical Guide for Parents, Teachers, and Therapists - Hardcover

Lindberg, Barbro

Hardcover

ISBN 10: 0889370338 ISBN 13: 9780889370333

Publisher: Hogrefe & Huber, 1997

Synopsis

Rett Syndrome is a severe neurological disorder whose cause is currently unknown. It leads to a variety of problems, often involving retardation, serious motor handicaps, epileptic seizures and difficulties with communication. The syndrome is found only in girls, and usually only becomes noticable during the second year of life. The disorder is estimated to occur in one out of every 10,000 female births worldwide, but as the characteristics of the problem are becoming more widely known, new cases are being reported at an increasing rate. This work on Rett Syndrome attempts to explain the problem and the implications for the individuals involved, their parents, teachers and those who work with them. As no cure is available yet, medical science has little to offer in the way of help to the families involved. This book provides practical insights and techniques for those working with this problem.

About this title

Review

Christopher J. Graver, PhD(Western State Hospital) **Description** As the title suggests, this book addresses Rett syndrome and the complex array of symptoms and behaviors from an educational perspective. The author has spent extensive time with these patients. **Purpose** This book is intended to provide general information about the general development and course of Rett syndrome, signs and symptoms, and treatment consideration for individuals who have this disease. The second edition is intended to expand the coverage of this disease through chapters on intelligence and education, learning and communication, and sensory environments. **Audience** It is intended for individuals who work with those who have Rett syndrome, including caregivers, educators, psychologists, occupational and physical therapists, and physicians. **Features** A brief overview of the stages of Rett syndrome is presented, followed by a look at the functional abilities of the 39 girls involved in the study. The book then progresses to signs and symptoms of Rett syndrome. The author provides a unique and personal approach to this disease by giving examples of patients'behaviors which illustrate the range of possibilities with this syndrome. There are very practical solutions offered for treating and managing the symptoms of this syndrome, which stem from the author's experience in working with these patients. In addition to providing management strategies, the author also presents strategies for enriching and improving the quality of life for these patients. The book ends with a few examples of interview forms that may be helpful when discussing the patient with a parent, caregiver, or teacher. Regrettably, this book is lacking in empirical references that may have helped to solidify some of this information. For example, in the interacting and communicating section, the recent article by Stauder, Smeets, van Mil, and Curfs ("The development of visual and auditory processing in Rett syndrome: An ERP study." Brain Development, in press.) would have added a scientific understanding to the behavioral observations of the author. For a second edition, the limited number of updated references is disappointing. **Assessment** From a practical perspective, this book delivers useful observations on clinical signs, symptoms, and behaviors in Rett syndrome, and does so in a personal manner with specific examples from patients. In addition, the suggestions for the management of problematic behaviors and enrichment of the patients' lives are insightful. Readers approaching the book in this hands-on manner will find it valuable; readers hoping to gain a deeper scientific understanding of Rett syndrome, however, may walk away feeling unfulfilled. ----------------------------------------------------------- Weighted Numerical Score: 77 - 3 Stars

Edition details

• Publisher: Hogrefe & Huber
• Publication date: 1997
• Language: English
• ISBN 10: 0889370338
• ISBN 13: 9780889370333
• Binding: Hardcover
• Edition number: 4
• Number of pages: 184